Qhov txawv ntawm Neurofibroma thiab Schwannoma

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Qhov txawv ntawm Neurofibroma thiab Schwannoma
Qhov txawv ntawm Neurofibroma thiab Schwannoma

Video: Qhov txawv ntawm Neurofibroma thiab Schwannoma

Video: Qhov txawv ntawm Neurofibroma thiab Schwannoma
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Qhov Tseem Ceeb Qhov txawv - Neurofibroma vs Schwannoma

Schwanommas thiab neurofibromas yog cov qog uas tshwm sim los ntawm cov ntaub so ntswg. Qhov sib txawv tseem ceeb ntawm neurofibroma thiab Schwannoma yog tias neurofibromas yog tsim los ntawm ntau hom hlwb xws li Schwann hlwb, fibroblasts, thiab lwm yam thaum schwannomas muaj tsuas yog Schwann hlwb.

Neurofibromas yog ib pab pawg benign ntawm cov hlab ntsha hauv cov hlab ntsha uas muaj ntau yam hauv qhov xwm txheej. Schwannomas, ntawm qhov tod tes, yog ib pab pawg benign ntawm cov qog uas tshwm sim los ntawm cov hlab ntsha peripheral uas yog tus cwj pwm los ntawm lub xub ntiag ntawm Schwann hlwb nyob rau hauv ntau theem ntawm kev sib txawv.

Neurofibroma yog dab tsi?

Neurofibromas yog ib pab pawg benign ntawm cov hlab ntsha hlwb. Cov no muaj ntau qhov sib txawv hauv qhov ntau dua li schwannomas thiab yog ua los ntawm neoplastic Schwann hlwb uas sib xyaw nrog perineurial hlwb xws li fibroblasts.

Neurofibromas tuaj yeem tshwm sim raws li cov kab mob sib cais lossis theem nrab rau neurofibromatosis. Nyob ntawm tus qauv kev loj hlob ntawm cov qog neuromas tau muab faib ua peb pawg loj.

Nyob rau hauv daim tawv nqaij tawv nqaij

Cov no feem ntau yog pedunculated thiab tuaj yeem yog ib leeg lossis ntau yam.

YDiffuse Neurofibromas

Cov ntau yam no feem ntau cuam tshuam nrog neurofibromatosis hom 1 thiab yog tus cwj pwm los ntawm qhov muaj cov quav hniav zoo li cov kab mob uas tau nce siab ntawm daim tawv nqaij.

YPlexiform Neurofibromas

Plexiform neurofibromas tshwm sim nyob rau hauv ob qho tib si superficial lossis tob qauv ntawm lub cev.

Qhov txawv tseem ceeb - Neurofibroma vs Schwannoma
Qhov txawv tseem ceeb - Neurofibroma vs Schwannoma

Daim duab 01: Neurofibromas

Morphology ntawm Neurofibromas

Localized cutaneous neurofibromas muaj nyob rau ntawm daim tawv nqaij lossis hauv cov rog subcutaneous. Lawv yog cov kab mob zoo-delineated thiab feem ntau yog encapsulated. Diffuse neurofibromas zoo ib yam li cov kab mob qog nqaij hlav hauv cheeb tsam hauv ntau yam. Dab tsi txawv lawv los ntawm cov kab mob cutaneous yog lawv cov qauv infiltrative ntawm kev loj hlob. Muaj Meissner's corpuscle zoo li qhov tshwm sim vim muaj kev sau ntawm cov hlwb. Plexiform neurofibromas loj hlob nyob rau hauv cov hlab ntsha fascicles thiab nthuav lawv thaum entrapping cov axons txuam.

Yog tias neurofibromas cuam tshuam nrog neurofibromatosis cov neeg mob tuaj yeem muaj lwm yam xws li,

  • kawm nyuaj
  • Malignant transformation
  • Scoliosis
  • Fibrodysplasia

Kev tshem tawm cov neurofibromas yuav tsum tau ua yog tias lawv ua cov tsos mob.

Schwannoma yog dab tsi?

Schwannomas yog ib pab pawg benign ntawm cov qog uas tshwm sim los ntawm cov hlab ntsha peripheral uas yog tus cwj pwm los ntawm lub xub ntiag ntawm Schwann hlwb nyob rau hauv ntau theem ntawm kev sib txawv.

Schwannomas tuaj yeem pom hauv neurofibromatosis hom 2. Ib qho kev koom tes ntawm cov qog no nrog kev hloov pauv ntawm NF2 noob tau tsim.

Morphology

Schwannomas tau zoo demarcated thiab encapsulated masses uas abut lub paj hlwb tsis muaj tiag invading rau hauv lub paj hlwb. Lawv muaj qhov xoob thiab ntom ntom ntawm cov ntaub so ntswg hu ua Antoni A thiab Antoni B feem. Lwm qhov tshwj xeeb yog qhov muaj Verocay lub cev uas yog thaj chaw tsis muaj nuclear uas nyob nruab nrab ntawm thaj tsam ntawm palisading nuclei.

Qhov txawv ntawm Neurofibroma thiab Schwannoma
Qhov txawv ntawm Neurofibroma thiab Schwannoma

Daim duab 02: Schwannoma

Tshuaj Kho Mob

  • Feem ntau ntawm cov tsos mob yog vim yog compression ntawm cov qauv uas nyob ib sab xws li lub hlwb thiab qaum qaum. Nws tuaj yeem muaj cov yam ntxwv ntawm qhov siab intracranial siab thiab ntau yam kev puas siab puas ntsws nyob ntawm thaj chaw uas tau compressed.
  • Ib feem ntau ntawm schwannomas tshwm sim hauv lub kaum sab xis cerebellopontine. Cov paj hlwb tseem ceeb suav nrog cov paj hlwb ntawm lub ntsej muag, cov hlab ntsha vestibulocochlear, thiab cov hlab ntsha glossopharyngeal tshwm sim los ntawm thaj av no. Yog li ntawd, ib tug compression ntawm cov hlab ntsha tuaj yeem ua rau cov hlab ntsha cranial palsies. Tinnitus thiab hnov tsis hnov lus yog cov yam ntxwv ntawm acoustic neuromas.

Kev phais mob ntawm cov qog yog qhov kev kho kom zoo.

Dab tsi yog qhov zoo sib xws ntawm Neurofibroma thiab Schwannoma?

  • Ob leeg yog cov qog nqaij hlav zoo li tshwm sim hauv cov ntaub so ntswg.
  • Muaj kev sib koom tes muaj zog nrog neurofibromatosis
  • Kev phais ntawm cov qog yog qhov kev kho mob rau ob hom qog.

Qhov txawv ntawm Neurofibroma thiab Schwannoma yog dab tsi?

Neurofibroma vs Schwannoma

Neurofibromas yog ib pawg benign ntawm cov qog hlwb. Schwanommas yog ib pab pawg benign ntawm cov qog uas tshwm sim los ntawm cov hlab ntsha peripheral uas yog tus cwj pwm los ntawm lub xub ntiag ntawm Schwann hlwb nyob rau hauv ntau theem ntawm kev sib txawv.
Cov no muaj ntau qhov sib txawv hauv qhov xwm txheej dua li Schwanommas thiab yog tsim los ntawm cov hlwb neoplastic Schwann uas sib xyaw nrog perineurial hlwb xws li fibroblasts. Schwanommas yog tsim los ntawm Schwann hlwb hauv ntau theem ntawm kev sib txawv.
Tshuaj kho mob

Yog tias neurofibromas cuam tshuam nrog neurofibromatosis cov neeg mob tuaj yeem muaj lwm yam xws li,

  • kawm nyuaj
  • Malignant transformation
  • Scoliosis
  • Fibrodysplasia
  • Cov tsos mob feem ntau yog vim muaj kev sib txuam ntawm cov qauv uas nyob ib sab xws li lub hlwb thiab qaum qaum. Nws tuaj yeem muaj cov yam ntxwv ntawm qhov siab intracranial siab thiab ntau yam kev puas siab puas ntsws nyob ntawm thaj chaw uas tau compressed.
  • Ib feem ntau ntawm schwannomas tshwm sim hauv lub kaum sab xis cerebellopontine. Cov paj hlwb tseem ceeb suav nrog cov paj hlwb ntawm lub ntsej muag, cov hlab ntsha vestibulocochlear, thiab cov hlab ntsha glossopharyngeal tshwm sim los ntawm thaj av no. Yog li ntawd, qhov compression ntawm cov hlab ntsha no tuaj yeem ua rau muaj kev cuam tshuam ntawm cov hlab ntsha cranial palsies.
  • Tinnitus thiab hnov tsis hnov lus yog cov yam ntxwv ntawm acoustic neuromas.

Summary – Schwanommas vs Neurofibromas

Schwanommas thiab neurofibromas yog cov qog uas tshwm sim los ntawm cov ntaub so ntswg. Schwanommas muaj tsuas yog Schwann hlwb tab sis neurofibromas muaj ntau hom cell xws li Schwann hlwb thiab fibroblasts. Qhov no yog qhov sib txawv loj ntawm neurofibromas thiab Schwanommas.

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