Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome

Cov txheej txheem:

Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome
Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome

Video: Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome

Video: Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome
Video: Qhov Txawv Ntawm Lus Hmoob Thiab Lus Mab Mawb 2024, Lub Xya hli ntuj
Anonim

Qhov Tseem Ceeb Qhov txawv - Myasthenia Gravis vs Lambert Eaton Syndrome

Myasthenia gravis yog ib qho kab mob autoimmune uas tshwm sim los ntawm kev tsim cov tshuaj tiv thaiv kab mob uas thaiv kev sib kis ntawm impulses hla cov kab mob neuromuscular. Lambert Eaton syndrome yog ib qho kev tshwm sim paraneoplastic ntawm me me cell carcinomas uas yog vim muaj qhov tsis xws luag acetylcholinesterase tso tawm ntawm lub neuromuscular hlws ris. Myasthenia gravis yog tus kab mob autoimmune thaum Lambert Eaton syndrome yog paraneoplastic syndrome. Qhov no yog qhov txawv ntawm myasthenia gravis thiab Lambert Eaton syndrome.

Myasthenia Gravis yog dab tsi?

Myasthenia gravis yog ib qho kab mob autoimmune uas tshwm sim los ntawm kev tsim cov tshuaj tiv thaiv kab mob uas thaiv kev sib kis ntawm impulses hla cov kab mob neuromuscular. Cov tshuaj tiv thaiv no khi rau postsynaptic Ach receptors, tiv thaiv kev khi ntawm Ach hauv synaptic cleft rau cov receptors. Cov poj niam muaj tsib zaug cuam tshuam los ntawm tus mob no ntau dua li txiv neej. Muaj kev koom tes tseem ceeb nrog rau lwm yam kab mob autoimmune xws li mob caj dab rheumatoid, SLE, thiab autoimmune thyroiditis. Concurrent thymic hyperplasia tau pom.

Tshuaj Kho Mob

  • Muaj qhov tsis muaj zog ntawm cov leeg nqaij limb, cov leeg sab nraud, thiab cov leeg pob txha
  • muaj zog thiab hloov pauv ntawm cov leeg tsis muaj zog
  • Tsis mob leeg
  • Lub plawv tsis cuam tshuam tab sis cov leeg ua pa tuaj yeem cuam tshuam
  • Reflexes kuj fatigable
  • Diplopia, ptosis, thiab dysphagia
Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton syndrome
Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton syndrome

Daim duab 01: Myasthenia Gravis

Kev tshawb nrhiav

  • Anti ACh receptor antibodies hauv cov ntshav
  • Tensilon kuaj qhov twg koob tshuaj edrophonium raug tswj hwm, uas ua rau muaj kev txhim kho ib ntus ntawm cov tsos mob uas kav ntev li 5 feeb
  • Kev Tshawb Fawb
  • ESR and CRP

Kev tswj hwm

  • Kev tswj hwm ntawm anticholinesterases xws li pyridostigmine
  • Immunosuppressants xws li corticosteroids tuaj yeem muab rau cov neeg mob uas tsis teb rau anticholinesterases
  • YThymectomy
  • Plasmapheresis
  • YIntravenous immunoglobulins

Dab tsi yog Lambert Eaton Syndrome?

Lambert Eaton Syndrome yog ib qho kev tshwm sim paraneoplastic ntawm cov qog nqaij hlav me me vim yog qhov tsis xws luag acetylcholinesterase tso tawm ntawm cov hlab ntsha neuromuscular.

Tshuaj Kho Mob

  • Cov leeg nqaij tsis muaj zog qee zaus nrog lub ntsej muag lossis lub plab tsis muaj zog
  • Tsis muaj kev cuam tshuam
Qhov txawv tseem ceeb - Myasthenia Gravis vs Lambert Eaton Syndrome
Qhov txawv tseem ceeb - Myasthenia Gravis vs Lambert Eaton Syndrome

Daim duab 02: Cov Kab Mob Me Me ntawm lub ntsws

Diagnosis

EMG thiab rov ua dua qhov kev txhawb nqa yog siv rau hauv kev lees paub ntawm kev kuaj mob

Kev tswj hwm

3,4 Diaminopyiridine tau raug pov thawj tias muaj txiaj ntsig.

Dab tsi yog qhov zoo sib xws ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome?

Ob yam kab mob no yog vim muaj qhov tsis xws luag hauv kev sib kis ntawm cov hlab ntsha hauv cov hlab ntsha ntawm theem ntawm cov kab mob neuromuscular

Qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome yog dab tsi?

YMyasthenia Gravis vs Lambert Eaton syndrome

Myasthenia gravis yog ib qho mob autoimmune yam ntxwv los ntawm kev tsim cov tshuaj tiv thaiv kab mob uas thaiv kev sib kis ntawm impulses hla cov hlab ntsha neuromuscular. Lambert Eaton Syndrome yog ib qho kev tshwm sim paraneoplastic ntawm cov qog nqaij hlav me me uas yog vim muaj cov acetylcholinesterase tsis raug tso tawm ntawm cov hlab ntsha neuromuscular.
hom
Myasthenia gravis yog ib yam kab mob autoimmune. Lambert Eaton syndrome yog tus mob paraneoplastic.
Tshuaj kho mob
  • Tsis muaj zog hauv cov leeg nqaij limb, cov leeg nqaij sab nraud, thiab cov leeg pob txha
  • Fatigability thiab fluctuation hais txog cov leeg tsis muaj zog
  • Tsis mob leeg
  • Lub plawv tsis cuam tshuam, tab sis cov leeg ua pa tuaj yeem cuam tshuam
  • Reflexes kuj fatigable
  • Diplopia, ptosis, thiab dysphagia

Cov leeg nqaij tsis muaj zog qee zaus nrog lub ntsej muag lossis lub plab tsis muaj zog

Tsis muaj kev cuam tshuam

Kev kuaj mob
  • Anti ACh receptor antibodies hauv cov ntshav
  • Tensilon test
  • Kev Tshawb Fawb
  • ESR and CRP
EMG thiab rov ua dua tshiab
  • Kev tswj hwm ntawm anticholinesterases xws li pyridostigmine
  • Immunosuppressants xws li corticosteroids tuaj yeem muab rau cov neeg mob uas tsis teb rau anticholinesterases
  • YThymectomy
  • Plasmapheresis
  • YIntravenous immunoglobulins
3, 4 Diaminopyiridine tau raug pov thawj tias muaj txiaj ntsig zoo hauv kev tswj hwm ntawm Lambert Eaton syndrome.

Summary – Myasthenia Gravis vs Lambert Eaton Syndrome

Myasthenia gravis yog ib qho kab mob autoimmune uas tshwm sim los ntawm kev tsim cov tshuaj tiv thaiv kab mob uas thaiv kev sib kis ntawm impulses hla cov kab mob neuromuscular. Lambert Eaton syndrome yog ib qho kev tshwm sim paraneoplastic ntawm me me cell carcinomas uas yog vim muaj qhov tsis xws luag acetylcholinesterase tso tawm ntawm lub neuromuscular hlws ris. Raws li tau hais hauv lawv cov lus txhais, myasthenia gravis yog kab mob autoimmune thaum Lambert Eaton syndrome yog ib qho mob paraneoplastic. Qhov no yog qhov txawv ntawm Myasthenia Gravis thiab Lambert Eaton syndrome.

Download PDF Version of Myasthenia Gravis vs Lambert Eaton Syndrome

Koj tuaj yeem rub tawm PDF version ntawm kab lus no thiab siv nws rau offline hom phiaj raws li cov ntawv sau tseg. Thov download PDF version ntawm no Qhov txawv Ntawm Myasthenia Gravis thiab Lambert Eaton Syndrome

Pom zoo: